CHENNAI, August 2, 2012 /PRNewswire/ --
MIOT Hospitals performs successful surgery on a 14-year-old boy in Chennai who was suffering from several disorders including the breast bone pushing the whole heart to left side of the chest thereby compressing the lungs, a hole in the heart, a bulge in the heart's biggest blood vessel and a leaky valve.
Case Scenario:
A 14-year-old boy from Mumbai who was diagnosed with Noonan's syndrome was admitted at MIOT Hospitals, Chennai on July 14, 2012. Noonan's syndrome is an autosomal congenital disorder considered to be a type of dwarfism. The features include narrowing of heart valve, hole in the heart, depressed breast bone (pectus excavatum), webbed neck and a flat nasal bridge. It occurs 1 in 1000 child births.
This boy was diagnosed to have a large hole in the heart (ASD) as a child, when was 4 years old. He was having progressive breathlessness and recently when he went for the treatment for the hole in the heart, he was found to have a large aneurysm of the aorta with leak in the aortic valve. The local doctors from Mumbai told him that it is extremely difficult to do the operation and he was advised to go abroad to get it done.
This combination of aneurysm of the aorta with leak in the aortic valve and a hole in the heart has not been reported before. T
he young boy in addition had a chest wall abnormality called pectus excavatum in which the breast bone has gone very deep and this has pushed the heart completely to the left side of the chest.
Recently, he was having breathlessness and was not able to sleep properly and was referred to MIOT Hospitals for surgery since it could not be done anywhere else.
Normally, open heart surgery is performed by cutting the breast bone because the heart is pushed behind. Done this way, the operation is easy to perform. But in case of this young boy, since the heart was totally on the left side of the chest, it was impossible to do this operation through the midline. The team of cardio thoracic surgeons at MIOT Hospitals searched extensively in the literature to find out which is the best way of doing this operation, but could not find a single case report of this combination of disease.
PR Newswire